Affiliations: Department of Pediatric Neurology, Indira Gandhi
Institute of Child Health, Bangalore, Karnataka, India | Department of Neuroradiology, National Institute of
Mental Health and Neurosciences, Bangalore, Karnataka, India | Department of Pediatrics, Indira Gandhi Institute of
Child Health, Bangalore, Karnataka, India | Department of Neurology, Bangalore Medical College and
research Institute, Bangalore, India | Department of Anatomy, Kempegowda Institute of Medical
Science, Bangalore, India
Note: [] Correspondence: Dr. Vykuntaraju K. Gowda, Bangalore Child
Neurology and Rehabilitation Center, HANS complex, 8/A 1st Main 1st Cross,
Manuvana, Near Adhichunchanagiri Choultry, Vijaynagar, Bangalore, 560040,
Karnataka, India. Tel.: +91 80 23301212, +91 9535212556; Fax: +91 80 26541799;
E-mail: drknvraju@ hotmail.com, drknvraju@yahoo.co.in
Abstract: Hemiconvulsion-hemiplegia-epilepsy syndrome is an uncommon
consequence of prolonged focal febrile convulsive seizures in infancy and early
childhood. We report two cases of hemiconvulsion-hemiplegia-epilepsy syndrome
who presented acutely and had striking neuroimaging findings suggestive of
diffuse cytotoxic edema confined to one hemisphere as documented by magnetic
resonance imaging, including extensive diffusion weighted imaging abnormalities
in both the cases.
Keywords: HHE syndrome, developmental delay, focal febrile status epilepticus
