Affiliations: Department of Radiology, University of Malaya Medical
Center, Kuala Lumpur, Malaysia | Department of Pathology, University of Malaya Medical
Center, Kuala Lumpur, Malaysia | Department of Pediatric Oncology, University of Malaya
Medical Center, Kuala Lumpur, Malaysia | Department of Pediatric Surgery, University of Malaya
Medical Center, Kuala Lumpur, Malaysia
Note: [] Correspondence: Dr. Emily Siew Ling Mah, Department of
Radiology, University of Malaya Medical Center, Lembah Pantai, 59100 Kuala
Lumpur, Malaysia. Tel.: +60 3 79494603; Fax: +60 3 79492878; E-mail:
aling7@yahoo.com
Abstract: Primary intracranial primitive neuroectodermal tumors are rare
malignant small cell embryonal neoplasms of neuroectodermal origin, accounting
for approximately 2.5% of childhood brain tumors and 0.46% of those in adults.
There are very few reported cases of extracranial metastases from these tumors.
We report a very rare case of primary intracranial primitive neuroectodermal
tumor with metastasis to the lungs.